OverviewSickle cell anemia is one of a group of inherited disorders known as sickle cell disease. It affects the shape of red blood cells, which carry oxygen to all parts of the body. Show
Red blood cells are usually round and flexible, so they move easily through blood vessels. In sickle cell anemia, some red blood cells are shaped like sickles or crescent moons. These sickle cells also become rigid and sticky, which can slow or block blood flow. There's no cure for most people with sickle cell anemia. Treatments can relieve pain and help prevent complications associated with the disease. SymptomsSigns and symptoms of sickle cell anemia usually appear around 6 months of age. They vary from person to person and may change over time. Signs and symptoms can include:
When to see a doctorSee your health care provider right away if you or your child has symptoms of sickle cell anemia. Because children with sickle cell anemia are prone to infections, which often start with a fever and can be life-threatening, seek prompt medical attention for a fever greater than 101.5 F (38.5 C). Seek emergency care for symptoms of stroke, which include:
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PreventionIf you carry the sickle cell trait, seeing a genetic counselor before trying to conceive can help you understand your risk of having a child with sickle cell anemia. A genetic counselor can also explain possible treatments, preventive measures and reproductive options. Which actions would the nurse take when admitting a client having sickle cell crisis?A newly admitted client has sickle cell crisis. The nurse is planning care based on assessment of the client.. Place her in Trendelenburg position.. Decrease the rate of IV infusion.. Administer oxygen per nasal cannula.. Increase the rate of the IV infusion.. Which prevention strategy should the nurse suggest to help prevent future sickle cell crises?Sickle cell disease is an inherited blood disorder affecting red blood cells.. Get enough oxygen.. Drink plenty of fluids.. Avoid getting over-heated or getting very cold.. Avoid getting infections, and quickly treat infections when you do get them.. See a primary care doctor.. Which drug is not recommended for treating pain during sickle cell disease episodes?Morphine is considered the drug of choice for the treatment of acute sickle cell pain (Table 2), whereas meperidine (Demerol, Sanofi-Synthelabo) should be avoided because of the increased risk of seizures in patients with renal dysfunction, which can occur in patients with SCD.
Which should the nurse prepare for as a priority in the management of a client in sickle cell crisis?The priority is to prevent and minimize bleeding. Oxygenation in answer C is important, but platelets do not carry oxygen. Answers B and D are of lesser priority and are incorrect in this instance. Answer C is correct.
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